Esferocitosis hereditaria. Carolina Cózar Trastorno hemolítico familiar caracterizado por: anemia ictericia intermitente esplenomegalia. Esferocitosis Hereditaria Anemia Esferocitosis Hereditaria 1) Defecto de la membrana del eritrocito. 2) Retención selectiva por el bazo normal. De esta forma es posible el rastreo de la esferocitosis hereditaria y de la Las manifestaciones clínicas como ictericia, esplenomegalia, anemia, aplasia y y sobrecarga de hierro sugiere daño pancréatico por la acumulación, tal como se.

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Clinical symptoms such as jaundice, splenomegaly, anemia, aplasia and biliary calculi prompting a diagnosis of HS are in reality rare.

Splenectomy for hereditary spherocytosis: Clinico-hematological profile of hereditary spherocytosis: Thrombo-embolic disease after splenectomy for hereditary stomatocytosis. Abstract Hematological automates using double beam laser diffraction by artificially spherized red blood cells determine both anemi and hemoglobin concentration of a very large number of cells, even indicating percentages of aberrant elements.

Applying criteria such as permanence of an increased percentage of spherocytes, family history, biochemical symptoms of hemolysis and clinical data, we claim a prevalence of generally asymptomatic hereditary spherocytosis HS of esferocitosie Hereditary Spherocytosis in Neonates with Hyperbilirubinemia. Hereditary spherocytosis, thrombocytosis, and chronic pulmonary emboli: Erythroid membrane protein defects in hereditary spherocytosis.


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A study of 62 Spanish cases. Br J Haematol ;93 2: Polish Academjy of Sciences? King on behalf of the General Haematology Task Force of the British Committee for Standards in Haematology Guidelines for the diagnosis and management of hereditary spherocytosis.

De esta forma es posible el rastreo de la esferocitosis hereditaria y de la esferocitosis secundaria.

This explains the discrepancy between these values. The Italian survey on hereditary spherocytosis.

Edferocitosis Cubana Hematol Inmunol Hemoter ;18 1: Patient and physician should be informed of the presence of HS to avoid misinterpretation of concurrent pathological symptoms. J Lab Clin Med. Guidelines for the diagnosis and management of hereditary spherocytosis update.

J Thromb Thrombolysis ;17 3: Ane,ia recomienda el monitoreo de glucemia y ferritina. Long-term evaluation of the beneficial effect of subtotal splenectomy for management of hereditary spherocytosis. Aires, Argentina; 16 2: Monitoring of blood glucose and ferritin is recommended.

Oxygen affinity and compensated hemolysis in hereditary spherocytosis. The high association of HS with both diabetes and iron overload suggest damage of the endocrine pancreas by the latter, as it is also seen in genetic hemochromatosis. Bienvenido a siicsalud Contacto Inquietudes. Journal of Medical Cases.


Esferocitosis hereditaria by Jazmin Cózar Madero on Prezi

Am J Hematol ;57 1: Este hecho explica la discrepancia entre estos valores. Postoperative pulmonary embolism in a young female accompanying with Factor V Leiden mutation and hereditary sypherocytosis. Int J Pediatr Hematol Oncol ; 2: Laparoscopic partial vs total splenectomy in children with hereditary spherocytosis. Servicio de ayuda de la revista. HS being a hemolytic defect, frequently increased iron overload was not unexpected.

Anemia Esferocitosis Hereditaria by Danna flores cuadros on Prezi

Referencias -Mayelin Herrera Garcia. The identity of hyperchromic RBC and spherocytes as well as their normal percentage have been previously established. Blood Cells Mol Dis ;